Liver Transplant in a Patient With Hemophagocytic Lymphohistiocytosis

Soy E. H. A., Alam H., Olcay L., Baris Z., Yildirim S., Torgay A., ...Daha Fazla

EXPERIMENTAL AND CLINICAL TRANSPLANTATION, cilt.17, ss.226-229, 2019 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 17
  • Basım Tarihi: 2019
  • Doi Numarası: 10.6002/ect.mesot2018.p80
  • Dergi Adı: EXPERIMENTAL AND CLINICAL TRANSPLANTATION
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.226-229
  • Eskişehir Osmangazi Üniversitesi Adresli: Hayır

Özet

Hemophagocytic lymphohistiocytosis is a rare and life-threatening systemic disease that can cause hepatic infiltration and present as acute liver failure. Here, we report a case of a 3-year-old pediatric patient who presented with acute liver failure and hepatic encephalopathy secondary to hemophagocytic lymphohistiocytosis. She had left lateral segment liver transplant from her father. After 27 months, she had bone marrow transplant from her sister. At the time of reporting (36 months after liver transplant), she showed normal liver function and blood peripheral counts. We found that liver transplant can be a curative treatment for this type of rare disorder, not only to improve the quality of life but also to prolong survival.