Emergency Difficult Airway Management in a Patient with Severe Epidermolysis Bullosa

ÖZKAN A. S., Kayhan G., AKBAŞ S., Kacmaz O., DURMUŞ M.

TURKISH JOURNAL OF ANAESTHESIOLOGY AND REANIMATION, cilt.44, sa.5, ss.270-272, 2016 (ESCI) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 44 Sayı: 5
  • Basım Tarihi: 2016
  • Doi Numarası: 10.5152/tjar.2016.49260
  • Dergi Adı: TURKISH JOURNAL OF ANAESTHESIOLOGY AND REANIMATION
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.270-272
  • Anahtar Kelimeler: Epidermolysis bullosa, nasal fiberoptic intubation, difficult airway, DYSTROPHICA
  • Eskişehir Osmangazi Üniversitesi Adresli: Hayır

Özet

Epidermolysis bullosa (EB) is a rare disease characterised by vesiculobullous lesions with minimal trauma to the skin and mucous membranes. Bleeding, scar tissue, contractures, oedema and lesions that can spread throughout the body can cause a difficult airway and vascular access in patients with EB. Therefore, anaesthetic management in patients with EB is a major problem even for experienced anaesthesiologists. Herein, we report a case of difficult airway management in a patient diagnosed with severe EB who presented for emergency tracheostomy because of respiratory failure under general anaesthesia.