Akademik Veri Yönetim Sistemi
TURKISH JOURNAL OF UROLOGY, cilt.33, sa.2, ss.213-217, 2007 (ESCI)
Introduction: Renal lymphangiomatosis is a rare developmental malformation resulting in the development of cystic masses in the peri-pelvic or peri-renal areas. The lymphatic tissue around the kidney fails to establish a normal communication with the rest of the lymphatic system. This pathology leads to dilatation of the lymphatic channels around the kidneys that causes formation of unilocular or multilocular cystic mass. This condition is usually bilateral but it might be unilateral and can be focal when smaller intrarenal lymphatics are obstructed. Frequently, this pathology can be confused with other renal cystic diseases. Up to date, this anomaly has been reported in radiology literature and to our knowledge it has not been published in Turkish urology literature, yet. The aim of this study was to discuss five cases of renal lymhangiomatosis with the relevant the literature. Materials and Methods: Between December 2003 and January 2007, a total of five patients diagnosed as renal lymphangiomatosis were included into the study. All patients were evaluated with physical examination, routine hematologic and biochemical analysis, urinalysis, urinary ultrasonography, computerized tomography, CT urography and MR, if needed. Results: The median age of the patients was 48.8 (41-54) years and the median follow-up period was 1.9 (9 ay-3 years) years. Three of the patients were female. Family history was unremarkable in all patients. Three patients were referred to our clinic from other clinics. The other two patients admitted to our clinic with complaints of bilaterally flank pain. After radiologic evaluation, bilateral renal lymhangiomatosis were detected in all patients. Only in two patients, costovertebral angle tenderness was detected. There was no history of haematuria, dysuria or oliguria. Routine hematologic and biochemical analysis were within normal ranges in all cases. On radiologic evaluation renal paranchymes were detected as normal. In addition there was no hydroureteronephrosis. Conclusion: Although, it is a relatively rarely seen congenital lymphatic disorder of the kidney, renal lymphangiomatosis should be considered in the differential diagnosis of renal cystic diseases and hydronephrosis.