Two siblings diagnosed with epidermodysplasia verrusiformis: Case report Epidermodysplasia verrusiformis
GUNCEL PEDIATRI-JOURNAL OF CURRENT PEDIATRICS, cilt.17, sa.3, ss.435-441, 2019 (ESCI, Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 17 Sayı: 3
- Basım Tarihi: 2019
- Doi Numarası: 10.4274/jcp.2019.0038
- Dergi Adı: GUNCEL PEDIATRI-JOURNAL OF CURRENT PEDIATRICS
- Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus
- Sayfa Sayıları: ss.435-441
- Eskişehir Osmangazi Üniversitesi Adresli: Evet
Özet
Epidermodisplasia verrusiformis (Lewandowsky Lutz syndrome) is a rare, autosomal recessive genodermatosis characterized by a defect in cellular immunity and increased susceptibility to Human Papillomavirus infection. Typical clinical findings include pityriasis versicolor-like macules, flat wart-like papules, psoriasiform red papules, and pigmented keratotic lesions resembling seborrheic keratosis. Cutaneous malignancies can develop on sun-exposed regions.