Schwannomas are the tumors originating from Schwann cells of the nerve sheath which covers peripheral nerves. Generally the initial symptom is radicular pain due to irritation or compression of the relevant nerve root which increases severely at night. Occipital neuralgic pain as a presenting symptom of these patients is extremely rare. In the vast of the cases, the etiology can not be determined. The tumors affecting the 2nd or 3rd cervical dorsal roots appear as the etiological factors of occipital neuralgia. In this paper we present a case of upper cervical Schwannoma presenting with occipital neuralgia and to our knowledge only one case has been reported previously in the literature to date.